Double inlet left ventricle (DILV) is a very rare congenital heart defect in which the child develops only one ventricle — the pumping chamber of the heart. individuals with DILV may have other heart problems as well, such as coarctation of the aorta, pulmonary atresia, or pulmonary valve stenosis.

Symptoms may include a bluish color to the skin and lips (cyanosis) due to low blood oxygen, failure to gain weight and grow, pale skin, poor feeding because of tiring easily, sweating, swollen legs or abdomen, and trouble breathing.

This fetal condition is diagnosed by ultrasound so that special preparations can be made for optimum care at delivery.